Year: 2023 | Month: October-December | Volume: 8 | Issue: 4 | Pages: 67-70
DOI: https://doi.org/10.52403/ijshr.20230410
Erasmus Syndrome: A Rare Case Report of Systemic Sclerosis with Silicosis and Progressive Massive Fibrosis
Dr. Hargurdas Singh1, Dr. Nishant Kumar Singh 2
1Senior Resident, Department of Internal Medicine, Sri Guru Ram Das Institute of Medical Sciences & Research, Amritsar, India
2Senior Resident, Department of Internal Medicine, Indira Gandhi Institute of Medical Sciences, Patna, India
Corresponding Author: Dr. Nishant Kumar Singh
ABSTRACT
Erasmus Syndrome is a rare disorder that is characterized by the development of systemic sclerosis after significantly prolonged exposure to silica with or without silicosis. Systemic Sclerosis is a multisystem autoimmune disease with vascular changes, inflammation, and diffuse tissue fibrosis. We report a case of Erasmus syndrome in a 45-year-old male who worked in the marble industry. The patient presented with difficulty in breathing, skin tightening, joint pain, Raynaud’s phenomenon, microstomia, and progressive massive fibrosis.
Keywords: Erasmus Syndrome, Systemic Sclerosis, Silicosis, Progressive Massive Fibrosis